Keratosis lichenoides chronica: treatment with bath-PUVA.
نویسندگان
چکیده
Sir, Keratosis lichenoides chronica (KLC) is a rare and chronic skin disease characterized by erythemas, keratotic and lichenoid papules, arranged in a linear pattern (1) and seborrhoeic-like scaling lesions on the trunk and limbs (1, 2). The lesions are slowly progressive with no tendency to heal and are resistant to most therapeutic modalities. Typical locations are the limbs, face, nails, palms, soles and mucous membranes (2, 3). No preference has been described for sex or age. Since 1972 the term “keratosis lichenoides chronica”, suggested by Margolis, has been generally accepted for this condition, except in France, where it is named “lichenoid tri-keratosis” (1). KLC is commonly considered either as a distinct entity or as a rare manifestation of lichen planus. Here we describe 2 young adults with typical clinical features of KLC and propose bath-psoralen plus ultraviolet light A (bath-PUVA) therapy as a potentially useful treatment for this rare disease, which is resistant to most classical anti-inflammatory therapies.
منابع مشابه
Keratosis lichenoides chronica successfully treated with isotretinoin and methotrexate
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ورودعنوان ژورنال:
- Acta dermato-venereologica
دوره 87 2 شماره
صفحات -
تاریخ انتشار 2007